Inicio Radiología RM en la enfermedad de Legg-Calve-Perthes. Comentario · Articles in press · Current Issue · Archive · Supplements · Most Often Read. Legg-Calve-Perthes disease (LCPD) occurs when blood supply to the ball of the thighbone in the hip (femoral head) is disrupted. Without an adequate blood. A number sign (#) is used with this entry because of evidence that Legg-Calve- Perthes disease (LCPD), a form of avascular necrosis of the femoral head (ANFH ;.

Author: Yok Ganris
Country: Senegal
Language: English (Spanish)
Genre: Automotive
Published (Last): 14 November 2014
Pages: 62
PDF File Size: 12.49 Mb
ePub File Size: 2.33 Mb
ISBN: 672-9-96024-769-1
Downloads: 45278
Price: Free* [*Free Regsitration Required]
Uploader: Arasar

Children affected by LCP disease often display uneven gait and limited range of motion, and they experience mild to severe pain in the groin area. Avascular necrosis of the femoral head is a debilitating disease that usually leads to destruction of the hip joint in the third to fifth decade of life Mont and Hungerford, Legg-Calve-Perthes disease usually involves just one hip. However, no evidence of this has been found; over the years, many theories have been published, but none has stood up to professional research.

Clinical description The initial symptoms are usually a limping gait, pain in the hip, thigh or knee, and a reduced range of hip engermedad. Inherited vascular pattern of the femoral head and neck as a predisposing factor to Legg-Calve-Perthes disease. How important is this topic for clinical practice?

Children who have had Legg-Calve-Perthes disease are at higher risk of developing hip arthritis in adulthood — particularly if the hip joint heals in an abnormal shape.

Check this box if you wish to receive capve copy of your message. Previous article Next article.

Azar FM, et al. If MRI or bone scans are necessary, a positive diagnosis relies upon patchy areas of vascularity to the capital femoral epiphysis the developing femoral head. Mayo Foundation for Medical Education and Research; He has nearly full abduction. To keep the ball part of the joint as round as possible, doctors may use a variety of treatments that keep it snug in the socket portion of the calvr.


Histology femoral epiphysis and physis exhibit areas of disorganized cartilage with areas of hypercellularity and fibrillation.

Accessed March 27, L7 – years in practice. Orthop Clin N Am. International Perthes Study Group.

By using this site, you agree to the Terms of Use and Privacy Policy. In 8 patients with this disorder, they found protein C deficiency in 3 and protein S deficiency in 1. Nelson Textbook of Pediatrics.


The socket acts as a mold for the fragmented femoral head as it heals. What is the dw most appropriate step in treatment? J Bone Joint Surg Am. Please consider making a donation now and again in the future.

Legg-Calve-Perthes Disease

The documents contained in this web site are presented for information purposes only. LCP disease is a vascular restrictive condition of idiopathic nature. In some cases, some activity can cause severe irritation or inflammation of the damaged area, including standing, walking, running, kneeling, or stooping repeatedly for an extended period of time.

Presence of a radiolucency in the shape of a V in the lateral portion of the epiphysis Gage sign. But if the ball is no longer round after it heals, it can cause pain and stiffness. It is generally accepted that one or more infarctions of the femoral head due to interruption of vascular supply eventually cause the deformity, however, there are several theories concerning the cause rnfermedad this interruption.

We need long-term secure funding to provide you cslve information that you need at your fingertips. Avascular necrosis of the capital femoral epiphysis C Mutations in the COL2A1 gene 12qq Genetics do not appear to be a determining factor, but a deficiency of blood factors with anticoagulant property used to disperse blood clots may lead to blockages in the vessels supplying the joint.

In some cases, pain is felt in the unaffected hip and leg, [ citation needed ] due to the children favoring their injured side and placing the majority of their weight on their “good” leg.


Based on radiographic cresent sign. Articles needing additional references from July All articles needing additional references Infobox medical condition new All articles with unsourced statements Articles with unsourced statements from August Articles with unsourced statements from May Articles with unsourced statements from February While running and high-impact sports are not recommended during treatment for Perthes disease, children can remain active through a variety of other activities that limit mechanical stress on the hip joint.

Bilateral Perthes, which means both hips are affected, should always be investigated thoroughly to rule out multiple epiphyseal dysplasia. Perhhes – June Pages A similar phenomenon has been oerthes in ankylosing spondylitis and in congenital dislocation of the hip. Leroux J, et al. The main aim ehfermedad treatment is to contain the femoral head within the acetabulum, either using an abduction brace or through surgical calvee femoral or pelvic osteotomy. The active phase of the disease can last for several years, and during this phase the femoral head becomes partially or completely necrotic and gradually deformed.

The child perthee then engage in activities appropriate for a six-year- old child, but lacking the bone strength of an older child, these activities may lead to flattening or fracture of the hip joint.

It is most commonly seen in persons aged three to 12 years, with a median of six years of age.

SRJ is a prestige metric based on the idea that not all citations are the same. Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted.

File under: Sex